• Norries disease
• Coats diesase in young people= x linked FEVR
• FEVR
• IP
• ?ROP
• Coats adults=?x linked FEVR

D Kinshuck, 
partly from notes from a lecture given by Prof T Moore, 2011

• bilateral retinal detachments at birth = Norries
• x linked 2/3 chance mother is a carrier
• Genes/details
• http://www.norriedisease.org/    
• condition

If the condition can be detected early, laser treatment at birth can prevent the retinal detachment and further visual loss see.

Essentially the condition is like ROP (retinopathy of prematurity)

• at birth the peripheral retinal has not been vascularised
• this retina becomes ischaemic after birth
• neovascularisation and then fibrosis develops
• the treatment is laser of the ischaemic retina before the vascularisation....laser shortly after birth

Norries disease and other proliferative vitreoretinopathies need urgent laser treatment of the ischaemic retina.
Avastin may have a role.

• Review 2011
• Coats diesase in young people is probably this condtion, x linked FEVR
• clinical